open access

Vol 25, No 1 (2018)
Original articles — Clinical cardiology
Published online: 2017-07-10
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What determines the quality of life of adult patients after Fontan procedure?

Monika Smaś-Suska, Natalia Dłużniewska, Piotr Weryński, Jacek Pająk, Wojciech Płazak, Maria Olszowska, Piotr Podolec, Lidia Tomkiewicz-Pająk
DOI: 10.5603/CJ.a2017.0078
·
Pubmed: 28695974
·
Cardiol J 2018;25(1):72-80.

open access

Vol 25, No 1 (2018)
Original articles — Clinical cardiology
Published online: 2017-07-10

Abstract

Background: Despite the low early mortality of Fontan procedures, Fontan patients are prone to vari­ous cardiac and extra-cardiac complications in the long term. This may influence patient perception of their health and outcome. The aim of the study was to assess the relationship of multi-organ compli­cations and physical efficiency with self-reported health-related quality of life (QOL) in adult Fontan patients.

Methods: Quality of life was assessed with the Short Form-36 questionnaire. Laboratory tests were done together with echocardiography, plethysmography, and cardiopulmonary exercise test.

Results: The QOL was poorer in patients than in control subjects. The physical characteristics of patients correlated with dynamic ventilatory parameters, heart rate at the peak of exercise, alanine aminotransferase and albumin level.

Conclusions: Liver impairment and chronotropic incompetence during exercise are associated with poor QOL in patients after Fontan procedure. In these patient, hepatic, pulmonary and cardiac functions should be carefully monitored. (Cardiol J 2018; 25, 1: 72–80)

Abstract

Background: Despite the low early mortality of Fontan procedures, Fontan patients are prone to vari­ous cardiac and extra-cardiac complications in the long term. This may influence patient perception of their health and outcome. The aim of the study was to assess the relationship of multi-organ compli­cations and physical efficiency with self-reported health-related quality of life (QOL) in adult Fontan patients.

Methods: Quality of life was assessed with the Short Form-36 questionnaire. Laboratory tests were done together with echocardiography, plethysmography, and cardiopulmonary exercise test.

Results: The QOL was poorer in patients than in control subjects. The physical characteristics of patients correlated with dynamic ventilatory parameters, heart rate at the peak of exercise, alanine aminotransferase and albumin level.

Conclusions: Liver impairment and chronotropic incompetence during exercise are associated with poor QOL in patients after Fontan procedure. In these patient, hepatic, pulmonary and cardiac functions should be carefully monitored. (Cardiol J 2018; 25, 1: 72–80)

Get Citation

Keywords

adult Fontan patients, quality of life, SF-36, exercise tolerance, pulmonary function test, multiorgan complications

About this article
Title

What determines the quality of life of adult patients after Fontan procedure?

Journal

Cardiology Journal

Issue

Vol 25, No 1 (2018)

Pages

72-80

Published online

2017-07-10

DOI

10.5603/CJ.a2017.0078

Pubmed

28695974

Bibliographic record

Cardiol J 2018;25(1):72-80.

Keywords

adult Fontan patients
quality of life
SF-36
exercise tolerance
pulmonary function test
multiorgan complications

Authors

Monika Smaś-Suska
Natalia Dłużniewska
Piotr Weryński
Jacek Pająk
Wojciech Płazak
Maria Olszowska
Piotr Podolec
Lidia Tomkiewicz-Pająk

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