open access

Vol 20, No 1 (2013)
Case Reports
Published online: 2013-02-07
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Long-term survivor diagnosed with arrhythmogenic right ventricular cardiomyopathy/dysplasia

Katsuro Kashima, Yasuhiro Tanaka, Kazuyo Kawabata, Rumiko Eura, Takashi Yamane, Kazuhiko Nakamura, Mitsuharu Nomoto
DOI: 10.5603/CJ.2013.0013
·
Cardiol J 2013;20(1):83-86.

open access

Vol 20, No 1 (2013)
Case Reports
Published online: 2013-02-07

Abstract

The subject was a 70 year-old man who survived for 31 years after being diagnosed with right ventricular cardiomyopathy, having undergone right ventricular (RV) aneurysmectomy at the age of 39. His arrhythmia and syncopal attacks were effectively abolished after the original aneurysmectomy. Although he frequently suffered from right heart failure, hemodialysis improved his status. However, the patient died due to worsening anasarca caused by RV low output syndrome. Autopsy results indicated extensive replacement of the RV myocardium with fibrous and fatty tissues. This case suggests that patients with arrhythmogenic RV cardiomyopathy, but without left ventricular abnormalities and rapid ventricular arrhythmia, have a relatively favorable prognosis, although RV abnormalities may be progressive.

Abstract

The subject was a 70 year-old man who survived for 31 years after being diagnosed with right ventricular cardiomyopathy, having undergone right ventricular (RV) aneurysmectomy at the age of 39. His arrhythmia and syncopal attacks were effectively abolished after the original aneurysmectomy. Although he frequently suffered from right heart failure, hemodialysis improved his status. However, the patient died due to worsening anasarca caused by RV low output syndrome. Autopsy results indicated extensive replacement of the RV myocardium with fibrous and fatty tissues. This case suggests that patients with arrhythmogenic RV cardiomyopathy, but without left ventricular abnormalities and rapid ventricular arrhythmia, have a relatively favorable prognosis, although RV abnormalities may be progressive.
Get Citation

Keywords

right ventricular cardiomyopathy; prognosis; aneurysmectomy

About this article
Title

Long-term survivor diagnosed with arrhythmogenic right ventricular cardiomyopathy/dysplasia

Journal

Cardiology Journal

Issue

Vol 20, No 1 (2013)

Pages

83-86

Published online

2013-02-07

DOI

10.5603/CJ.2013.0013

Bibliographic record

Cardiol J 2013;20(1):83-86.

Keywords

right ventricular cardiomyopathy
prognosis
aneurysmectomy

Authors

Katsuro Kashima
Yasuhiro Tanaka
Kazuyo Kawabata
Rumiko Eura
Takashi Yamane
Kazuhiko Nakamura
Mitsuharu Nomoto

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