open access

Vol 45, No 2 (2013 Apr-Jun)
Case reports
Submitted: 2013-07-05
Accepted: 2013-07-05
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Anaesthesia in children with osteogenesis imperfecta — report of 14 general anaesthetics in three children

Ewa Górnik-Właszczuk, Jacek Majewski, Rafał Szczygieł, Andrzej Dusiel
DOI: 10.5603/AIT.2013.0019
·
Anaesthesiol Intensive Ther 2013;45(2):85-88.

open access

Vol 45, No 2 (2013 Apr-Jun)
Case reports
Submitted: 2013-07-05
Accepted: 2013-07-05

Abstract

Osteogenesis imperfecta is a rare, genetically inherited syndrome involving connective tissue. It results in extremely fragile bones and disorders of other organs and body systems. Children with osteogenesis imperfecta are susceptible to bone fractures and often require surgery and anaesthesia. We describe a series of 14 general anaesthetics in three patients suffering from this disease. In one of these cases, perioperative hyperthermia was observed. Anaesthetic management of osteogenesis imperfecta and a possible relationship between this syndrome and malignant and non-malignant hyperthermia are discussed.

Abstract

Osteogenesis imperfecta is a rare, genetically inherited syndrome involving connective tissue. It results in extremely fragile bones and disorders of other organs and body systems. Children with osteogenesis imperfecta are susceptible to bone fractures and often require surgery and anaesthesia. We describe a series of 14 general anaesthetics in three patients suffering from this disease. In one of these cases, perioperative hyperthermia was observed. Anaesthetic management of osteogenesis imperfecta and a possible relationship between this syndrome and malignant and non-malignant hyperthermia are discussed.

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Keywords

osteogenesis imperfecta, general anaesthesia; osteogenesis imperfecta, malignant hyperthermia

About this article
Title

Anaesthesia in children with osteogenesis imperfecta — report of 14 general anaesthetics in three children

Journal

Anaesthesiology Intensive Therapy

Issue

Vol 45, No 2 (2013 Apr-Jun)

Pages

85-88

DOI

10.5603/AIT.2013.0019

Bibliographic record

Anaesthesiol Intensive Ther 2013;45(2):85-88.

Keywords

osteogenesis imperfecta
general anaesthesia
osteogenesis imperfecta
malignant hyperthermia

Authors

Ewa Górnik-Właszczuk
Jacek Majewski
Rafał Szczygieł
Andrzej Dusiel

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