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Primary pleural synovial sarcoma: a rare cause of hemorrhagic pleural effusion
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Abstract
Primary pleural synovial sarcoma (PPSS) is a rare malignant pleural tumor comprising < 1% of all primary lung malignancies. Primary pleural mesothelioma (PPM) has many similar features that may cause a diagnostic dilemma due to overlapping clinical and histopathological features. We present the case of a young male with recurrent hemorrhagic pleural effusion without any obvious lung mass who was diagnosed with PPSS. This rare entity must be considered with a high index of suspicion while evaluating pleural tumors.
Abstract
Primary pleural synovial sarcoma (PPSS) is a rare malignant pleural tumor comprising < 1% of all primary lung malignancies. Primary pleural mesothelioma (PPM) has many similar features that may cause a diagnostic dilemma due to overlapping clinical and histopathological features. We present the case of a young male with recurrent hemorrhagic pleural effusion without any obvious lung mass who was diagnosed with PPSS. This rare entity must be considered with a high index of suspicion while evaluating pleural tumors.
Keywords
hemorrhagic; immunohistochemistry; pleural effusion; sarcoma; synovial
About this articleTitle
Primary pleural synovial sarcoma: a rare cause of hemorrhagic pleural effusion
Journal
Advances in Respiratory Medicine
Issue
Article type
Case report
Published online
2020-10-30
DOI
10.5603/ARM.a2020.0147
Keywords
hemorrhagic
immunohistochemistry
pleural effusion
sarcoma
synovial
Authors
Subodh Kumar
Kashyap Goyal
Ritisha Bhatt
Saloni Bansal
Mayank Mishra
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