open access

Vol 82, No 3 (2014)
CASE REPORTS
Submitted: 2014-04-30
Accepted: 2014-04-30
Get Citation

A 24-year-old male patient with pulmonary veno-occlusive disease — case report

Edyta Ćwiek, Marcelina Przemęcka, Jerzy Marczak, Jan Kuś, Renata Langfort, Paweł Górski
DOI: 10.5603/PiAP.2014.0032
·
Pneumonol Alergol Pol 2014;82(3):271-275.

open access

Vol 82, No 3 (2014)
CASE REPORTS
Submitted: 2014-04-30
Accepted: 2014-04-30

Abstract

Pulmonary veno-occlusive disease (PVOD) is a rare cause of severe pulmonary hypertension characterised by poor prognosis. We report the case of a 24-year-old male patient with increasing dyspnea and exercise intolerance treated with calcium channel blockers and glucocorticosteroids, due to suspicion of pulmonary hypertension and interstitial lung disease, until lung biopsy was performed and a diagnosis of PVOD was established on the basis of the histological analysis of the lung biopsy sample. This case highlights that pulmonary veno-occlusive disease is a disorder that is difficult to diagnose and resistant to medical treatment, which is particularly poor prognostic factor. Due to poor response to medical therapy and high mortality in patients with PVOD, understanding the pathogenesis, differentiation with pulmonary arterial hypertension and the search for a new methods of treatment should be the key challenges for modern medicine.

Abstract

Pulmonary veno-occlusive disease (PVOD) is a rare cause of severe pulmonary hypertension characterised by poor prognosis. We report the case of a 24-year-old male patient with increasing dyspnea and exercise intolerance treated with calcium channel blockers and glucocorticosteroids, due to suspicion of pulmonary hypertension and interstitial lung disease, until lung biopsy was performed and a diagnosis of PVOD was established on the basis of the histological analysis of the lung biopsy sample. This case highlights that pulmonary veno-occlusive disease is a disorder that is difficult to diagnose and resistant to medical treatment, which is particularly poor prognostic factor. Due to poor response to medical therapy and high mortality in patients with PVOD, understanding the pathogenesis, differentiation with pulmonary arterial hypertension and the search for a new methods of treatment should be the key challenges for modern medicine.

Get Citation

Keywords

pulmonary veno-occlusive disease, pulmonary arterial hypertension, idiopathic pulmonary arterial hypertension, lung biopsy

About this article
Title

A 24-year-old male patient with pulmonary veno-occlusive disease — case report

Journal

Advances in Respiratory Medicine

Issue

Vol 82, No 3 (2014)

Pages

271-275

DOI

10.5603/PiAP.2014.0032

Bibliographic record

Pneumonol Alergol Pol 2014;82(3):271-275.

Keywords

pulmonary veno-occlusive disease
pulmonary arterial hypertension
idiopathic pulmonary arterial hypertension
lung biopsy

Authors

Edyta Ćwiek
Marcelina Przemęcka
Jerzy Marczak
Jan Kuś
Renata Langfort
Paweł Górski

Important: This website uses cookies. More >>

The cookies allow us to identify your computer and find out details about your last visit. They remembering whether you've visited the site before, so that you remain logged in - or to help us work out how many new website visitors we get each month. Most internet browsers accept cookies automatically, but you can change the settings of your browser to erase cookies or prevent automatic acceptance if you prefer.

Czasopismo Pneumonologia i Alergologia Polska dostęne jest również w Ikamed - księgarnia medyczna

Wydawcą serwisu jest "Via Medica sp. z o.o." sp.k., ul. Świętokrzyska 73, 80–180 Gdańsk

tel.:+48 58 320 94 94, faks:+48 58 320 94 60, e-mail: viamedica@viamedica.pl