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Severe hypoxemic respiratory insufficiency in a patient with hepato-pulmonary syndrome coexisting with interstitial lung disease of unknown etiology
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Abstract
The coexistence of the interstitial lung disease and respiratory failure is rarely associated with extrapulmonary pathology. In patients with liver cirrhosis, hypoxemia may develop in the course of hepato-pulmonary syndrome (HPS), but radiological pathology seen in the course of HPS is of vascular origin, and thus typically not classified as interstitial lung disease. We present a patient with severe hypoxemic respiratory insufficiency in whom hepato-pulmonary syndrome coexisted with interstitial lung disease of unknown etiology. The mechanisms of hypoxemia in the course of hepatic diseases and reasons of possible coincidence of lung and hepatic pathology are discussed.
Abstract
The coexistence of the interstitial lung disease and respiratory failure is rarely associated with extrapulmonary pathology. In patients with liver cirrhosis, hypoxemia may develop in the course of hepato-pulmonary syndrome (HPS), but radiological pathology seen in the course of HPS is of vascular origin, and thus typically not classified as interstitial lung disease. We present a patient with severe hypoxemic respiratory insufficiency in whom hepato-pulmonary syndrome coexisted with interstitial lung disease of unknown etiology. The mechanisms of hypoxemia in the course of hepatic diseases and reasons of possible coincidence of lung and hepatic pathology are discussed.
Keywords
liver cirrhosis, hepato-pulmonary syndrome, interstitial lung disease, respiratory failure
About this articleTitle
Severe hypoxemic respiratory insufficiency in a patient with hepato-pulmonary syndrome coexisting with interstitial lung disease of unknown etiology
Journal
Advances in Respiratory Medicine
Issue
Pages
267-272
Bibliographic record
Pneumonol Alergol Pol 2013;81(3):267-272.
Keywords
liver cirrhosis
hepato-pulmonary syndrome
interstitial lung disease
respiratory failure
Authors
Katarzyna Gorzkowska-Pasik
Elżbieta Wiatr
Barbara Burakowska
Urszula Nowicka
Jarosław Kober
Przemysław Malong
Piotr Pasik
Krystyna Folcik