open access

Vol 78, No 3 (2010)
CASE REPORTS
Published online: 2010-05-11
Submitted: 2013-02-22
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Interstitial lung disease in the course of the surfactant protein C deficiency coexisting with the primary humoral immunodeficiency - case study

Aleksandra Szczawińska-Popłonyk, Anna Bręborowicz, Renata Langfort
Pneumonol Alergol Pol 2010;78(3):244-247.

open access

Vol 78, No 3 (2010)
CASE REPORTS
Published online: 2010-05-11
Submitted: 2013-02-22

Abstract

The interstitial lung disease in children is a group of disorders heterogeneous in its etiology and pathogenesis. In differential diagnosis infectious, immunological and metabolic factors must be taken into consideration, as well as a genetically determined surfactant protein C deficiency. In the paper a case of interstitial lung disease in the course of the surfactant protein C deficiency coexisting with the primary humoral immunodeficiency is presented, with the discussion concerning clinical manifestation, radiological pattern, and histological findings.

Abstract

The interstitial lung disease in children is a group of disorders heterogeneous in its etiology and pathogenesis. In differential diagnosis infectious, immunological and metabolic factors must be taken into consideration, as well as a genetically determined surfactant protein C deficiency. In the paper a case of interstitial lung disease in the course of the surfactant protein C deficiency coexisting with the primary humoral immunodeficiency is presented, with the discussion concerning clinical manifestation, radiological pattern, and histological findings.
Get Citation

Keywords

interstitial pneumonia; surfactant protein C; immunodeficiency; children

About this article
Title

Interstitial lung disease in the course of the surfactant protein C deficiency coexisting with the primary humoral immunodeficiency - case study

Journal

Advances in Respiratory Medicine

Issue

Vol 78, No 3 (2010)

Pages

244-247

Published online

2010-05-11

Bibliographic record

Pneumonol Alergol Pol 2010;78(3):244-247.

Keywords

interstitial pneumonia
surfactant protein C
immunodeficiency
children

Authors

Aleksandra Szczawińska-Popłonyk
Anna Bręborowicz
Renata Langfort

References (11)
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