open access

Vol 78, No 6 (2010)
CASE REPORTS
Published online: 2010-10-29
Submitted: 2013-02-22
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Primary Sjögren’s syndrome with two extraglandular sites involvement - case report

Monika Szturmowicz, Ewelina Wilińska, Anna Paczek, Liliana Wawrzyńska, Lucyna Opoka, Juliusz Gątarek, Renata Langfort, Ewa Rowińska-Zakrzewska, Adam Torbicki
Pneumonol Alergol Pol 2010;78(6):445-450.

open access

Vol 78, No 6 (2010)
CASE REPORTS
Published online: 2010-10-29
Submitted: 2013-02-22

Abstract

Primary Sjögren’s Syndrome (pSS) is a chronic, slowly progressive inflammatory autoimmune disorder, characterised by lymphocytic infiltration of the exocrine glands, leading to decrease of glandular secretion. In 40–60% of pSS patients, extraglandular disease develops.
We present the case of a patient with two extraglandular sites involvement in the course of pSS manifesting with progressive respiratory and gastrointestinal symptoms.
Pneumonol. Alergol. Pol. 2010; 78, 6: 445-450

Abstract

Primary Sjögren’s Syndrome (pSS) is a chronic, slowly progressive inflammatory autoimmune disorder, characterised by lymphocytic infiltration of the exocrine glands, leading to decrease of glandular secretion. In 40–60% of pSS patients, extraglandular disease develops.
We present the case of a patient with two extraglandular sites involvement in the course of pSS manifesting with progressive respiratory and gastrointestinal symptoms.
Pneumonol. Alergol. Pol. 2010; 78, 6: 445-450
Get Citation

Keywords

primary Sjögren’s syndrome; diagnosis; lung disease; gastrointestinal disease

About this article
Title

Primary Sjögren’s syndrome with two extraglandular sites involvement - case report

Journal

Advances in Respiratory Medicine

Issue

Vol 78, No 6 (2010)

Pages

445-450

Published online

2010-10-29

Bibliographic record

Pneumonol Alergol Pol 2010;78(6):445-450.

Keywords

primary Sjögren’s syndrome
diagnosis
lung disease
gastrointestinal disease

Authors

Monika Szturmowicz
Ewelina Wilińska
Anna Paczek
Liliana Wawrzyńska
Lucyna Opoka
Juliusz Gątarek
Renata Langfort
Ewa Rowińska-Zakrzewska
Adam Torbicki

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