open access
Systemic mastocytosis associated with hematological neoplasm: a diagnostic challenge


- Department of Hematology and Bone Marrow Transplantation, Medical University of Silesia, Katowice, Poland
open access
Abstract
Abstract
Keywords
systemic mastocytosis, SM-AHN, eosinophilia


Title
Systemic mastocytosis associated with hematological neoplasm: a diagnostic challenge
Journal
Issue
Article type
Clinical vignette
Pages
46-47
Published online
2023-02-19
Page views
277
Article views/downloads
64
DOI
10.5603/AHP.a2023.0007
Bibliographic record
Acta Haematol Pol 2023;54(1):46-47.
Keywords
systemic mastocytosis
SM-AHN
eosinophilia
Authors
Karolina Chromik
Kinga Boral
Martyna Dworaczek
Grzegorz Helbig


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- Arber DA, Orazi A, Hasserjian R, et al. The 2016 revision to the World Health Organization classification of myeloid neoplasms and acute leukemia. Blood. 2016; 127(20): 2391–2405.
- Kluin-Nelemans HC, Reiter A, Illerhaus A, et al. Prognostic impact of eosinophils in mastocytosis: analysis of 2350 patients collected in the ECNM Registry. Leukemia. 2020; 34(4): 1090–1101.
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- Greiner G, Gurbisz M, Ratzinger F, et al. Digital PCR: a sensitive and precise method for D816V quantification in mastocytosis. Clin Chem. 2018; 64(3): 547–555.
- Jawhar M, Schwaab J, Naumann N, et al. Response and progression on midostaurin in advanced systemic mastocytosis: D816V and other molecular markers. Blood. 2017; 130(2): 137–145.