open access

Vol 23, No 1 (2017)
Case reports
Published online: 2017-05-12
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Successful closure of pulmonary artery aneurysm in a patient with Hughes-Stovin syndrome

Shokoufeh Hajsadeghi, Roozbeh Naghshin, Mehrdad Nikfam, Ali Pourmojarab, Sayfollah Abdi
DOI: 10.5603/AA.2017.0007
·
Acta Angiologica 2017;23(1):20-24.

open access

Vol 23, No 1 (2017)
Case reports
Published online: 2017-05-12

Abstract

Hughes-Stovin syndrome is a syndrome of unknown etiology characterized by thrombophlebitis and pulmonary aneurysms. Less than 40 cases have ever been reported in the English medical literature. We are reporting a 38-year-old man with a history of right ventricular thrombus and also deep vein thrombosis who presented with massive hemoptysis. Initial work-up revealed a round opacity on chest roentgenogram which later was diagnosed as a pulmonary artery aneurysm on subsequent imaging studies. Based on the history of thrombophlebitis with this newly diagnosed pulmonary artery aneurysm a diagnosis of Hughes-Stovin syndrome was made. The patient was treated with endovascular coiling of the aneurysm. A sixteen-month follow up was uneventful. To our knowledge, this is the first case of HSS ever reported from Iran and the fourth to have a cardiac chambers involvement in the course of the disease.

Abstract

Hughes-Stovin syndrome is a syndrome of unknown etiology characterized by thrombophlebitis and pulmonary aneurysms. Less than 40 cases have ever been reported in the English medical literature. We are reporting a 38-year-old man with a history of right ventricular thrombus and also deep vein thrombosis who presented with massive hemoptysis. Initial work-up revealed a round opacity on chest roentgenogram which later was diagnosed as a pulmonary artery aneurysm on subsequent imaging studies. Based on the history of thrombophlebitis with this newly diagnosed pulmonary artery aneurysm a diagnosis of Hughes-Stovin syndrome was made. The patient was treated with endovascular coiling of the aneurysm. A sixteen-month follow up was uneventful. To our knowledge, this is the first case of HSS ever reported from Iran and the fourth to have a cardiac chambers involvement in the course of the disease.

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Keywords

pulmonary artery, aneurysms, Hughes-Stovin syndrome

About this article
Title

Successful closure of pulmonary artery aneurysm in a patient with Hughes-Stovin syndrome

Journal

Acta Angiologica

Issue

Vol 23, No 1 (2017)

Pages

20-24

Published online

2017-05-12

DOI

10.5603/AA.2017.0007

Bibliographic record

Acta Angiologica 2017;23(1):20-24.

Keywords

pulmonary artery
aneurysms
Hughes-Stovin syndrome

Authors

Shokoufeh Hajsadeghi
Roozbeh Naghshin
Mehrdad Nikfam
Ali Pourmojarab
Sayfollah Abdi

References (21)
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