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Successful closure of pulmonary artery aneurysm in a patient with Hughes-Stovin syndrome
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Abstract
Hughes-Stovin syndrome is a syndrome of unknown etiology characterized by thrombophlebitis and pulmonary aneurysms. Less than 40 cases have ever been reported in the English medical literature. We are reporting a 38-year-old man with a history of right ventricular thrombus and also deep vein thrombosis who presented with massive hemoptysis. Initial work-up revealed a round opacity on chest roentgenogram which later was diagnosed as a pulmonary artery aneurysm on subsequent imaging studies. Based on the history of thrombophlebitis with this newly diagnosed pulmonary artery aneurysm a diagnosis of Hughes-Stovin syndrome was made. The patient was treated with endovascular coiling of the aneurysm. A sixteen-month follow up was uneventful. To our knowledge, this is the first case of HSS ever reported from Iran and the fourth to have a cardiac chambers involvement in the course of the disease.
Abstract
Hughes-Stovin syndrome is a syndrome of unknown etiology characterized by thrombophlebitis and pulmonary aneurysms. Less than 40 cases have ever been reported in the English medical literature. We are reporting a 38-year-old man with a history of right ventricular thrombus and also deep vein thrombosis who presented with massive hemoptysis. Initial work-up revealed a round opacity on chest roentgenogram which later was diagnosed as a pulmonary artery aneurysm on subsequent imaging studies. Based on the history of thrombophlebitis with this newly diagnosed pulmonary artery aneurysm a diagnosis of Hughes-Stovin syndrome was made. The patient was treated with endovascular coiling of the aneurysm. A sixteen-month follow up was uneventful. To our knowledge, this is the first case of HSS ever reported from Iran and the fourth to have a cardiac chambers involvement in the course of the disease.
Keywords
pulmonary artery, aneurysms, Hughes-Stovin syndrome
About this articleTitle
Successful closure of pulmonary artery aneurysm in a patient with Hughes-Stovin syndrome
Journal
Issue
Article type
Case report
Pages
20-24
Published online
2017-05-12
Page views
934
Article views/downloads
1405
DOI
10.5603/AA.2017.0007
Bibliographic record
Acta Angiologica 2017;23(1):20-24.
Keywords
pulmonary artery
aneurysms
Hughes-Stovin syndrome
Authors
Shokoufeh Hajsadeghi
Roozbeh Naghshin
Mehrdad Nikfam
Ali Pourmojarab
Sayfollah Abdi
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